Pediatric Craniosynostosis
Pediatric Craniosynostosis
What is Pediatric Craniosynostosis?
(crane-eo-sin-oh-STOW-sis)
The skull is formed by several separate bones. These skull bones are connected to one another by specialized structures called sutures. These sutures look like seams or spaces between the skull bones. The sutures are growth centers for the skull bones. Craniosynostosis is present when one or more of the sutures closes earlier than it should causing the skull to grow into an abnormal shape.
Babies' brains grow very quickly in the first two years of life. As the brain grows it stretches the sutures which signals the sutures to make new bone. The sutures allow the skull to enlarge and create just enough space for the brain. Normally, these sutures remain open until we reach adulthood, long after the brain and skull have stopped growing. Craniosynostosis causes a baby’s skull to be misshapen because the brain continues to grow at the same rate even if one or more sutures closes too early.
The remaining open sutures have to grow faster to make up for the closed suture. This extra growth causes a change in head shape. In some cases, the remaining open sutures can’t grow fast enough to keep up with the brain’s growth causing an abnormally high pressure in the skull, which can have negative effects on brain health. These include learning delays, blindness, and, rarely, death, if untreated.
Meet some of the patients we have treated to become familiar with what you can expect if your child is affected with craniosynostosis.
See craniosynostosis before and after photos
What are the different types of Pediatric Craniosynostosis?
Craniosynostosis can affect babies in two different ways.
Isolated craniosynostosis
Isolated craniosynostosis or non-syndromic (sin-DRŌ-mic) craniosynostosis is the closing of only one suture with no other associated health problems and is the most common kind of craniosynostosis. The types of isolated craniosynostosis are:
- Coronal Synostosis (Unilateral and Bilateral)
- Lambdoid Synostosis
- Metopic Synostosis
- Sagittal Synostosis
Syndromic craniosynostosis
Syndromes are when three or more medical problems occur in a recognizable pattern. When craniosynostosis is part of a syndrome there are usually two or more sutures closed too early. The types of syndromic craniosynostosis are:
Patients with craniosynostosis syndromes have multiple other medical problems and their skull and facial bones don’t grow normally. These additional problems makes their treatment of children with syndromic craniosynostosis much more complicated than that of patients with isolated craniosynostosis.
The needs and expected courses of treatment for these two groups of craniosynostosis patients are so different that we will discuss them in separate sections on this site.
What are the signs and symptoms of Pediatric Craniosynostosis?
- Abnormal feeling or disappearing fontanel (soft spot on the top of the head)
- Asymmetrical, misshapen skull
- Development of a raised, hard ridge along the skull
- Slow or no growth of the head as the baby grows
Pediatric Craniosynostosis Doctors and Providers
-
Alex Kane, MD Plastic and Craniofacial SurgeonDivision Director at Children's Health Associate Professor at UT Southwestern Medical CenterBoard Certification:
American Board of Plastic Surgery -
Rashmin Savani, MD NeonatologistDivision Director at Children's Health Professor at UT Southwestern Medical CenterRashmin Savani, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Noorjahan Ali, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterNoorjahan Ali, MD
Neonatologist
-
Chelsea Anderson, MD NeonatologistChelsea Anderson, MD
Neonatologist
Board Certification:
American Board of Pediatrics -
Dimitrios Angelis, MD NeonatologistDimitrios Angelis, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal,
American Board of Pediatrics -
Asya Asghar, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterAsya Asghar, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Kikelomo Babata, MD NeonatologistKikelomo Babata, MD
Neonatologist
-
Timothy Brannon, MD NeonatologistTimothy Brannon, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Luc Brion, MD NeonatologistProfessor at UT Southwestern Medical CenterLuc Brion, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Lina Chalak, MD NeonatologistLina Chalak, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Christina Chan, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterChristina Chan, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Vedanta Dariya, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterVedanta Dariya, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Christopher Derderian, MD Plastic and Craniofacial SurgeonAssistant Professor at UT Southwestern Medical CenterChristopher Derderian, MD
Plastic and Craniofacial Surgeon
Board Certification:
American Board of Plastic Surgery -
Becky Ennis, MD NeonatologistBecky Ennis, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Mackenzie Frost, MD NeonatologistMackenzie Frost, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Shamaila Gill, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterShamaila Gill, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
June Hu, MD NeonatologistJune Hu, MD
Neonatologist
-
Jawahar Jagarapu, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterJawahar Jagarapu, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Mambarambath Jaleel, MD NeonatologistMambarambath Jaleel, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Venkatakrishna Kakkilaya, MD NeonatologistVenkatakrishna Kakkilaya, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Sunny Kang, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterSunny Kang, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Vishal Kapadia, MD NeonatologistVishal Kapadia, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Athra Kaviani, MD NeonatologistAthra Kaviani, MD
Neonatologist
Board Certification:
American Board of Pediatrics -
Rachel Leon, MD NeonatologistRachel Leon, MD
Neonatologist
-
Imran Mir, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterImran Mir, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Julie Mirpuri-Hathiramani, MD NeonatologistJulie Mirpuri-Hathiramani, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Jessica Morse, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterJessica Morse, MD
Neonatologist
Board Certification:
American Board of Pediatrics -
Sujir Nayak, MD NeonatologistSujir Nayak, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Eric Ortigoza, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterEric Ortigoza, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Shalini Ramachandran, MD NeonatologistAssociate Professor at UT Southwestern Medical CenterShalini Ramachandran, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Joseph Schneider, MD NeonatologistJoseph Schneider, MD
Neonatologist
Board Certification:
American Board of Pediatrics -
James Seaward, MD Plastic and Craniofacial SurgeonAssistant Professor at UT Southwestern Medical CenterJames Seaward, MD
Plastic and Craniofacial Surgeon
Board Certification:
General Medical Council -
Julide Sisman, MD NeonatologistJulide Sisman, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Muraleedharan Sivarajan, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterMuraleedharan Sivarajan, MD
Neonatologist
Board Certification:
American Board of Pediatrics -
Kaili Stehel, MD NeonatologistAssociate Professor at UT Southwestern Medical CenterKaili Stehel, MD
Neonatologist
Board Certification:
American Board of Pediatrics -
Katherine Stumpf, MD NeonatologistKatherine Stumpf, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Phyllis Wan-Huen, MD NeonatologistPhyllis Wan-Huen, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Heather Weydig, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterHeather Weydig, MD
Neonatologist
-
Myra Wyckoff, MD NeonatologistAssociate Professor at UT Southwestern Medical CenterMyra Wyckoff, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal -
Sushmita Yallapragada, MD NeonatologistAssistant Professor at UT Southwestern Medical CenterSushmita Yallapragada, MD
Neonatologist
Board Certification:
American Board of Pediatrics/Neonatal-Perinatal
Frequently Asked Questions
-
When is a misshapen baby’s head not craniosynostosis?
Craniosynostosis is not the most common cause of an abnormal head shape. The most common cause by far is called positional or deformational plagiocephaly (play-GEE-oh-sef-alee).
-
How does a baby's skull change over time?
A baby’s skull has 6 major cranial sutures:
- The metopic suture
- Two coronal sutures
- The sagittal suture
- Two lambdoid sutures
The baby’s growing brain is what makes their skull grow. The growing brain does this by mechanically triggering growth signals in the sutures that leads to new bone formation and enlargement of the skull bones. This keeps the skull just large enough for the brain to fit perfectly. The brain more than triples in size during a child’s first 2 years of life. To make room for the brain, the skull must grow rapidly during this time, reaching 80% of its adult size by the age of 2 years. By age 5, the skull has grown to over 90% of the adult size. All sutures remain open until adulthood, except for the metopic suture which usually closes between 6 and 12 months of age.
A baby will have a misshapen head when one or more of the sutures closes too early. This usually happens prenatally, before the child is born. Again, the brain is growing very quickly at this age. The remaining open sutures must grow faster to create the space inside the skull that the closed suture was supposed to accommodate. This extra growth at the open sutures causes a misshapen head. The abnormal head shape created by craniosynostosis depends on which sutures are closed. Craniofacial surgeons can usually determine which suture(s) is closed when they examine the patient because the abnormal head shape that the closure of each suture produces is characteristic. In about 15 out of 100 cases, one closed suture results in the skull not growing fast enough to keep up with the rapid growth of the brain. This can be harmful to the health of the brain. The more closed sutures there are, the higher the likelihood that the skull will not be able to grow fast enough.