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Non-Rhabdomyosarcoma Soft Tissue Sarcoma

What are the different types of Non-Rhabdomyosarcoma Soft Tissue Sarcoma?

Some soft tissue tumors are categorized as non-rhabdomyosarcoma soft tissue sarcomas. This group makes up approximately 4% of all childhood cancers. These tumors are classified by the specific body parts they affect, and the cells differ in each type. The most common are blood vessel tumors, bone and cartilage tumors, connective tissue tumors, fat tissue tumors, nerve tumors and skin tumors.

Blood vessel tumors

Blood vessel tumors: may include angiosarcoma, which is a tumor that grows quickly in blood vessels. A specialized team at the Gill Center also sees children with benign blood vessel tumors or malformations.

Bone and cartilage tumors

Bone and cartilage tumors: may include chondrosarcoma which develops in the cartilage of the bone and is more common in adults.

Connective tissue tumors including:

  • Desmoid tumors, or aggressive fibromatosis, usually grow slowly and are unlikely to spread to other areas of the body. Children with the genetic condition familial adenomatous polyposis (FAP) are at higher risk for these connective tissue tumors.
  • Fibrosarcoma is typically found in children under age 4, especially in infants. Tumors tend to be large and grow quickly, but they usually do not spread to additional areas of the body. Patients with infantile fibrosarcoma are often referred to our Experimental Therapeutics Program for specialized care.
  • Infantile myofibromatosis is a rare condition that is most often identified in newborn babies. This tumor can spread to multiple sites in the body.

Fat tissue tumors

Fat tissue tumors: Also called liposarcoma may occur in children and is usually low-grade and grows slowly.

Nerve tumors

Nerve tumors: Malignant peripheral nerve sheath tumors grow in the covering of nerves outside the brain and spinal cord. Children with the genetic condition neurofibromatosis type 1 (NF1) are at higher risk for these tumors.

How is Non-Rhabdomyosarcoma Soft Tissue Sarcoma treated?

When a cancerous tumor is diagnosed, treatment may include chemotherapy to destroy the cancer cells depending on the tumor type. Surgery and radiation therapy are also possible treatment options. Your child’s physician will consider the size and location of the cancer, your child’s age and overall health, and whether the cancer has spread in planning the best treatment for your child. A number of families travel to our facility because of our leading therapies backed by the latest research.

Expert and experienced oncologists, surgeons and subspecialists staff Children’s Health. The Pauline Allen Gill Center for Cancer and Blood Disorders is a world-class and nationally recognized leader in pediatric cancer. If your child has been diagnosed with non-rhabdomyosarcoma soft tissue sarcoma or you want an expert second opinion, turn to pediatric tumor specialists who can manage complex cancer.