Pediatric Obstructed Hemivagina and Unilateral Renal Anomaly (OHVIRA) Syndrome

Pediatric Obstructed Hemivagina and Unilateral Renal Anomaly (OHVIRA) Syndrome

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Summary

Obstructed hemivagina and ipsilateral renal anomaly syndrome (OHVIRA) is a rare condition that causes a female to be born with a double uterus.

Expanded overview

Obstructed hemivagina and ipsilateral renal anomaly syndrome (OHVIRA) – sometimes known as Herlyn-Werner-Wunderlich syndrome – is a rare disorder in which a female baby is born with two uteruses. OHVIRA also causes renal agenesis, which means that one or both of the kidneys do not properly develop while the baby is in the womb.

If not properly treated, OHVIRA can lead to major complications such as endometriosis or infertility. 

Symptoms

Symptoms and signs of OHVIRA are:

  • Endometriosis (disorder in which tissue that normally lines the uterus grows outside the uterus)
  • Problems getting pregnant
  • Teenaged female who hasn't yet menstruated 

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